List of ICD-9 codes 320–389: diseases of the nervous system and sense organs

This is a shortened version of the sixth chapter of the ICD-9: Diseases of the Nervous System and Sense Organs. It covers ICD codes 320 to 389. The full chapter can be found on pages 215 to 258 of Volume 1, which contains all (sub)categories of the ICD-9. Volume 2 is an alphabetical index of Volume 1. Both volumes can be downloaded for free from the website of the World Health Organization.

In the ICD-9 system, a disease may have a cause listed in one chapter, and its manifestations listed in another. For example, Tuberculous meningitis is caused by a bacterial infection, and is therefore listed in Chapter 1, Infectious and parasitic diseases. However, as it results in a disorder of the nervous system, it is also listed in this chapter. An asterisk (*) means that a disease has an underlying cause which can be found elsewhere in the ICD. A code referring to such an underlying cause may be right next to the name, in parentheses, and marked with a dagger symbol of the Times New Roman font ( † ).

Inflammatory diseases of the central nervous system (320–326)

 *  Bacterial meningitis
 * Haemophilus meningitis
 * Pneumococcal meningitis
 * Streptococcal meningitis
 * Staphylococcal meningitis
 * * Tuberculous meningitis ( † )
 * * Meningococcal meningitis ( † )
 * * Meningitis in other bacterial diseases classified elsewhere
 * Meningitis due to other specified bacteria
 * Meningitis due to unspecified bacterium
 * * Meningitis due to other organisms
 * * Fungal meningitis (110–118 † )
 * * Meningitis due to Coxsackie virus ( † )
 * * Meningitis due to ECHO virus ( † )
 * * Meningitis due to herpes zoster virus ( † )
 * * Meningitis due to herpes simplex virus ( † )
 * * Meningitis due to mumps virus ( † )
 * * Meningitis due to lymphocytic choriomeningitis virus ( † )
 * * Meningitis due to other and unspecified viruses
 * * Other
 *  Meningitis of unspecified cause
 * Nonpyogenic meningitis
 * Eosinophilic meningitis
 * Chronic meningitis
 * Meningitis, unspecified
 *  Encephalitis, myelitis and encephalomyelitis
 * * Kuru ( † )
 * * Subacute sclerosing panencephalitis ( † )
 * * Poliomyelitis (045.– † )
 * * Arthropod-borne viral encephalitis (062-064 † )
 * * Other encephalitis due to infection
 * Encephalitis following immunization procedures
 * * Postinfectious encephalitis
 * * Toxic encephalitis
 * Other
 * Unspecified cause
 *  Intracranial and intraspinal abscess
 * Intracranial abscess
 * Intraspinal abscess
 * Of unspecified site
 *  Phlebitis and thrombophlebitis of intracranial venous sinuses
 *  Late effects of intracranial abscess or pyogenic infection

Hereditary and Degenerative diseases of the central nervous system (330–337)

 *  Cerebral degenerations usually manifest in childhood
 * Leucodystrophy
 * Cerebral lipidoses
 * * Cerebral degeneration in generalized lipidoses ( † )
 * * Cerebral degeneration of childhood in other diseases classified elsewhere
 * Other cerebral degenerations in childhood
 * Unspecified
 *  Other cerebral degenerations
 * Alzheimer's disease
 * Pick's disease
 * Senile degeneration of brain
 * Communicating hydrocephalus
 * Obstructive hydrocephalus
 * * Jakob-Creutzfeldt disease ( † )
 * * Progressive multifocal leucoencephalopathy ( † )
 * * Cerebral degeneration in other diseases classified elsewhere
 * Other cerebral degeneration
 * Unspecified
 *  Parkinson's disease
 * Paralysis agitans
 * Secondary Parkinsonism
 *  Other extrapyramidal disease and abnormal movement disorders
 * Other degenerative diseases of the basal ganglia
 * Essential and other specified forms of tremor
 * Myoclonus
 * Tics of organic origin
 * Huntington's chorea
 * Other choreas
 * Idiopathic torsion dystonia
 * Symptomatic torsion dystonia
 * Fragments of torsion dystonia
 * Other and unspecified
 *  Spinocerebellar disease
 * Friedreich's ataxia
 * Hereditary spastic paraplegia
 * Primary cerebellar degeneration
 * Other cerebellar ataxia
 * * Cerebellar ataxia in diseases classified elsewhere
 * Other
 * Unspecified
 *  Anterior horn cell disease
 * Werdnig-Hoffmann disease
 * Spinal muscular atrophy
 * Motor neurone disease
 * Other
 * Unspecified
 *  Other diseases of spinal cord
 * Syringomyelia and syringobulbia
 * Vascular myelopathies
 * * Subacute combined degeneration of spinal cord (,, † )
 * * Myelopathy in other diseases classified elsewhere
 * Other myelopathy
 * Unspecified diseases of spinal cord
 * Disorders of the autonomic nervous system
 * Idiopathic peripheral autonomic neuropathy
 * * Peripheral autonomic neuropathy in disorders classified elsewhere
 * Unspecified

Other disorders of the central nervous system (340–349)

 *  Multiple sclerosis
 *  Other demyelinating diseases of central nervous system
 * Neuromyelitis optica
 * Schilder's disease
 * Other
 * Unspecified
 *  Hemiplegia
 * Flaccid hemiplegia
 * Spastic hemiplegia
 * Unspecified
 *  Infantile cerebral palsy
 * Diplegic
 * Hemiplegic
 * Quadriplegic
 * Monoplegic
 * Infantile hemiplegia
 * Other
 * Unspecified
 *  Other paralytic syndromes
 * Quadriplegia
 * Paraplegia
 * Diplegia of upper limbs
 * Monoplegia of lower limb
 * Monoplegia of upper limb
 * Unspecified monoplegia
 * Cauda equina syndrome
 * Other
 * Unspecified
 *  Epilepsy
 * Generalized nonconvulsive epilepsy
 * Generalized convulsive epilepsy
 * Petit mal status
 * Grand mal status
 * Partial epilepsy, with impairment of consciousness
 * Partial epilepsy, without mention of impairment of consciousness
 * Infantile spasms
 * Epilepsia partialis continua
 * Other
 * Unspecified
 *  Migraine
 * Classical migraine
 * Common migraine
 * Variants of migraine
 * Other
 * Unspecified
 *  Cataplexy and narcolepsy
 *  Other conditions of brain
 * Cerebral cysts
 * Anoxic brain damage
 * Benign intracranial hypertension
 * Encephalopathy, unspecified
 * Compression of brain
 * Cerebral oedema
 * Other
 * Unspecified
 *  Other and unspecified disorders of the nervous system
 * Reaction to spinal or lumbar puncture
 * Nervous system complications from surgically implanted device
 * Disorders of meninges, not elsewhere classified
 * Other
 * Unspecified

Disorders of the peripheral nervous system (350–359)

 *  Trigeminal nerve disorders
 * * Post-herpetic trigeminal neuralgia ( † )
 * Other trigeminal neuralgia
 * Atypical face pain
 * Other
 * Unspecified
 *  Facial nerve disorders
 * Bell's palsy
 * Geniculate ganglionitis
 * Other
 * Unspecified
 *  Disorders of other cranial nerves
 * Disorders of olfactory &#91;1st&#93; nerve
 * Glossopharyngeal neuralgia
 * Other disorders of glossopharyngeal &#91;9th&#93; nerve
 * Disorders of pneumogastric &#91;10th&#93; nerve
 * Disorders of accessory &#91;11th&#93; nerve
 * Disorders of hypoglossal &#91;12th&#93; nerve
 * Multiple cranial nerve palsies
 * Unspecified
 *  Nerve root and plexus disorders
 * Brachial plexus lesions
 * Lumbosacral plexus lesions
 * Cervical root lesions, not elsewhere classified
 * Thoracic root lesions, not elsewhere classified
 * Lumbosacral root lesions, not elsewhere classified
 * Neuralgic amyotrophy
 * Phantom limb syndrome
 * Other
 * Unspecified
 *  Mononeuritis of upper limb and mononeuritis multiplex
 * Carpal tunnel syndrome
 * Other lesion of median nerve
 * Lesion of ulnar nerve
 * Lesion of radial nerve
 * Causalgia
 * Mononeuritis multiplex
 * Other
 * Unspecified
 *  Mononeuritis of lower limb
 * Lesion of sciatic nerve
 * Meralgia paraesthetica
 * Lesion of femoral nerve
 * Lesion of lateral popliteal nerve
 * Lesion of medial popliteal nerve
 * Tarsal tunnel syndrome
 * Lesion of plantar nerve
 * Other
 * Unspecified mononeuritis of lower limb
 * Mononeuritis of unspecified site
 *  Hereditary and idiopathic peripheral neuropathy
 * Hereditary peripheral neuropathy
 * Peroneal muscular atrophy
 * Hereditary sensory neuropathy
 * Refsum's disease
 * Idiopathic progressive polyneuropathy
 * Other
 * Unspecified
 *  Inflammatory and toxic neuropathy
 * Acute infective polyneuritis
 * * Polyneuropathy in collagen vascular disease
 * * Polyneuropathy in diabetes ( † )
 * * Polyneuropathy in malignant disease (140–208 † )
 * * Polyneuropathy in other diseases classified elsewhere
 * Alcoholic polyneuropathy
 * Polyneuropathy due to drugs
 * Polyneuropathy due to other toxic agents
 * Other
 * Unspecified
 *  Myoneural disorders
 * Myasthenia gravis
 * * Myasthenic syndromes in diseases classified elsewhere
 * Toxic myoneural disorders
 * Other
 * Unspecified
 *  Muscular dystrophies and other myopathies
 * Congenital hereditary muscular dystrophy
 * Hereditary progressive muscular dystrophy
 * Myotonic disorders
 * Familial periodic paralysis
 * Toxic myopathy
 * * Endocrine myopathy
 * * Symptomatic inflammatory myopathy
 * Other
 * Unspecified

Disorders of the eye and adnexa (360–379)

 *  Disorders of the globe
 * Purulent endophthalmitis
 * Other endophthalmitis
 * Degenerative disorders of globe
 * Hypotony of eye
 * Degenerated conditions of globe
 * Retained (old) intraocular foreign body, magnetic
 * Retained (old) intraocular foreign body, nonmagnetic
 * Other disorders of globe
 * Unspecified
 *  Retinal detachments and defects
 * Retinal detachment with retinal defect
 * Retinoschisis and retinal cysts
 * Serous retinal detachment
 * Retinal defects without detachment
 * Other forms of retinal detachment
 * Unspecified
 *  Other retinal disorders
 * * Diabetic retinopathy ( † )
 * Other background retinopathy and retinal vascular changes
 * Other proliferative retinopathy
 * Retinal vascular occlusion
 * Separation of retinal layers
 * Degeneration of macula and posterior pole
 * Peripheral retinal degenerations
 * Hereditary retinal dystrophies
 * Other retinal disorders
 * Unspecified
 *  Chorioretinal inflammations and scars and other disorders of choroid
 * Focal chorioretinitis and focal retinochoroiditis
 * Disseminated chorioretinitis and disseminated retinochoroiditis
 * Other and unspecified forms of chorioretinitis and retinochoroiditis
 * Chorioretinal scars
 * Choroidal degenerations
 * Choroidal haemorrhage and rupture
 * Choroidal detachment
 * Other disorders of choroid
 * Unspecified
 *  Disorders of iris and ciliary body
 * Acute and subacute iridocyclitis
 * Chronic iridocyclitis
 * Certain types of iridocyclitis
 * Unspecified iridocyclitis
 * Vascular disorders of iris and ciliary body
 * Degenerations of iris and ciliary body
 * Cysts of iris, ciliary body and anterior chamber
 * Adhesions and disruptions of iris and ciliary body
 * Other disorders of iris and ciliary body
 * Unspecified
 *  Glaucoma
 * Borderline glaucoma
 * Open-angle glaucoma
 * Primary angle-closure glaucoma
 * Corticosteroid-induced glaucoma
 * Glaucoma associated with congenital anomalies, with dystrophies and with systemic syndromes
 * Glaucoma associated with disorders of the lens
 * Glaucoma associated with other ocular disorders
 * Other glaucoma
 * Unspecified
 *  Cataract
 * Infantile, juvenile and presenile cataract
 * Senile cataract
 * Traumatic cataract
 * Cataract secondary to ocular disorders
 * Cataract associated with other disorders
 * After-cataract
 * Other cataract
 * Unspecified
 *  Disorders of refraction and accommodation
 * Hypermetropia
 * Myopia
 * Astigmatism
 * Anisometropia and aniseikonia
 * Presbyopia
 * Disorders of accommodation
 * Other
 * Unspecified
 *  Visual disturbances
 * Amblyopia ex anopsia
 * Subjective visual disturbances
 * Diplopia
 * Other disorders of binocular vision
 * Visual field defects
 * Colour vision deficiencies
 * Night blindness
 * Other visual disturbances
 * Unspecified
 *  Blindness and low vision
 * Blindness, both eyes
 * Blindness, one eye, low vision other eye
 * Low vision, both eyes
 * Unqualified visual loss, both eyes
 * Legal blindness, as defined in U.S.A.
 * Blindness, one eye
 * Low vision, one eye
 * Unqualified visual loss, one eye
 * Unspecified visual loss
 *  Keratitis
 * Corneal ulcer
 * * Dendritic keratitis ( † )
 * Other superficial keratitis without conjunctivitis
 * Certain types of keratoconjunctivitis
 * Other and unspecified keratoconjunctivitis
 * Interstitial and deep keratitis
 * Corneal neovascularization
 * Other forms of keratitis
 * Unspecified
 *  Corneal opacity and other disorders of cornea
 * Corneal scars and opacities
 * Corneal pigmentations and deposits
 * Corneal oedema
 * Changes of corneal membranes
 * Corneal degenerations
 * Hereditary corneal dystrophies
 * Keratoconus
 * Other corneal deformities
 * Other corneal disorders
 * Unspecified
 *  Disorders of conjunctiva
 * Acute conjunctivitis
 * Chronic conjunctivitis
 * Blepharoconjunctivitis
 * Other and unspecified conjunctivitis
 * Pterygium
 * Conjunctival degenerations and deposits
 * Conjunctival scars
 * Conjunctival vascular disorders and cysts
 * Other disorders of conjunctiva
 * Unspecified
 *  Inflammation of eyelids
 * Blepharitis
 * Chalazion
 * Noninfectious dermatoses of eyelid
 * * Infective dermatitis of eyelid of types resulting in deformity
 * * Other infective dermatitis of eyelid
 * * Parasitic infestation of eyelid
 * Other
 * Unspecified
 *  Other disorders of eyelids
 * Entropion and trichiasis of eyelid
 * Ectropion
 * Lagophthalmos
 * Ptosis of eyelid
 * Other disorders affecting eyelid function
 * Degenerative disorders of eyelids and periocular area
 * Other disorders of eyelid
 * Unspecified
 *  Disorders of lacrimal system
 * Dacryoadenitis
 * Other disorders of lacrimal gland
 * Epiphora
 * Acute and unspecified inflammation of lacrimal passages
 * Chronic inflammation of lacrimal passages
 * Stenosis and insufficiency of lacrimal passages
 * Other changes of lacrimal passages
 * Other disorders of lacrimal system
 * Unspecified
 *  Disorders of the orbit
 * Acute inflammation of orbit
 * Chronic inflammatory disorders of orbit
 * * Endocrine exophthalmos
 * Other exophthalmic conditions
 * Deformity of orbit
 * Enophthalmos
 * Retained (old) foreign body following penetrating wound of orbit
 * Other disorders of orbit
 * Unspecified
 *  Disorders of optic nerve and visual pathways
 * Papilloedema
 * Optic atrophy
 * Other disorders of optic disc
 * Optic neuritis
 * Other disorders of optic nerve
 * Disorders of optic chiasm
 * Disorders of other visual pathways
 * Disorders of visual cortex
 * Unspecified
 *  Strabismus and other disorders of binocular eye movements
 * Convergent concomitant strabismus
 * Divergent concomitant strabismus
 * Intermittent heterotropia
 * Other and unspecified heterotropia
 * Heterophoria
 * Paralytic strabismus
 * Mechanical strabismus
 * Other strabismus
 * Other disorders of binocular eye movements
 * Unspecified
 *  Other disorders of eye
 * Scleritis and episcleritis
 * Other disorders of sclera
 * Disorders of vitreous body
 * Aphakia and other disorders of lens
 * Anomalies of pupillary function
 * Nystagmus and other irregular eye movements
 * Other disorders of eye and adnexa
 * Unspecified

Diseases of the ear and mastoid process (380–389)

 *  Disorders of external ear
 * Perichondritis of pinna
 * Infective otitis externa
 * Other otitis externa
 * Noninfective disorders of pinna
 * Impacted cerumen
 * Acquired stenosis of external ear canal
 * Other disorders of external ear
 * Unspecified
 *  Nonsuppurative otitis media and Eustachian tube disorders
 * Acute nonsuppurative otitis media
 * Chronic serous otitis media
 * Chronic mucoid otitis media
 * Other and unspecified chronic nonsuppurative otitis media
 * Nonsuppurative otitis media, not specified as acute or chronic
 * Eustachian salpingitis
 * Obstruction of Eustachian tube
 * Patulous Eustachian tube
 * Other disorders of Eustachian tube
 * Unspecified Eustachian tube disorder
 *  Suppurative and unspecified otitis media
 * Acute suppurative otitis media
 * Chronic tubotympanic suppurative otitis media
 * Chronic atticoantral suppurative otitis media
 * Unspecified chronic suppurative otitis media
 * Unspecified suppurative otitis media
 * Unspecified otitis media
 *  Mastoiditis and related conditions
 * Acute mastoiditis
 * Chronic mastoiditis
 * Petrositis
 * Complications following mastoidectomy
 * Other
 * Unspecified mastoiditis
 *  Other disorders of tympanic membrane
 * Acute myringitis without mention of otitis media
 * Chronic myringitis without mention of otitis media
 * Perforation of tympanic membrane
 * Other
 * Unspecified
 *  Other disorders of middle ear and mastoid
 * Tympanosclerosis
 * Adhesive middle ear disease
 * Other acquired abnormality of ear ossicles
 * Cholesteatoma of middle ear and mastoid
 * Other
 * Unspecified
 *  Vertiginolls syndromes and other disorders of vestibular system
 * Ménière's disease
 * Other and unspecified peripheral vertigo
 * Vertigo of central origin
 * Labyrinthitis
 * Labyrinthine fistula
 * Labyrinthine dysfunction
 * Other disorders of labyrinth
 * Unspecified vertiginous syndromes and labyrinthine disorders
 *  Otosclerosis
 * Otosclerosis involving oval window, nonobliterative
 * Otosclerosis involving oval window, obliterative
 * Cochlear otosclerosis
 * Other
 * Unspecified
 *  Other disorders of ear
 * Degenerative and vascular disorders of ear
 * Noise effects on inner ear
 * Sudden hearing loss, unspecified
 * Tinnitus
 * Other abnormal auditory perception
 * Disorders of acoustic nerve
 * Otorrhoea
 * Otalgia
 * Other
 * Unspecified
 *  Deafness
 * Conductive deafness
 * Sensorineural deafness
 * Mixed conductive and sensorineural deafness
 * Deaf mutism, not elsewhere classifiable
 * Other specified forms of deafness
 * Unspecified deafness