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Gerstmann-Sträussler-Scheinker syndrome

'Gerstmann-Sträussler-Scheinker Disease' http://www.merckmanuals.com/home/brain_spinal_cord_and_nerve_disorders/prion_diseases/gerstmann-str%C3%A4ussler-scheinker_disease.html?qt=&sc=&alt=

Gerstmann-Straussler-Scheinker Disease Gerstmann-Straussler-Scheinker Disease (GSS) is an extremely rare neurogenetic brain disorder. It is always inherited and is found in only a few families all over the world (NINDS ¶ 1) . The trait is an autosomal dominant trait, caused by a gene mutation. It is also in a group of heredity prion protein diseases. Many symptoms are associated with GSS like progressive ataxia, pyramidal signs, and even adult-onset dementia; they progress more as the disease progresses (Farlow, Nov. 1989) . This paper will give background information on GSS and why it’s such a rare disease.